CUX1基因在阵发性睡眠性血红蛋白尿症中通过调控自噬促进克隆增殖的分子机制研究

81770110
2017
H0802.红细胞与相关疾病
付蓉
面上项目
主任医师
天津医科大学
53万元
阵发性睡眠性血红蛋白尿症;克隆增殖;自噬;CUX1基因
2018-01-01到2021-12-31
  • 中英文摘要
  • 结题摘要
  • 结题报告
  • 项目成果
  • 项目参与人
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序号 标题 类型 作者
1 多发性骨髓瘤微小残留病检测的研究进展 期刊论文 丁凯;付蓉
2 Bone Marrow Plasma Cytokine Signature Profiles in Severe Aplastic Anemia 期刊论文 Liu Bingnan;Shao Yuanyuan;Liu Zixuan;Liu Chunyan;Zhang Tian;Fu Rong
3 NK cells suppress CD8(+) T cell immunity via NKG2D in severe aplastic anemia 期刊论文 Chen Tong;Zhang Tian;Liu Chunyan;Wang ChaoMeng;Ding Shaoxue;Shao ZongHong;Fu Rong
4 Gene mutations associated with thrombosis detected by whole-exome sequencing in paroxysmal nocturnal hemoglobinuria 期刊论文 Li Liyan;Wang Honglei;Liu Hui;Liu Zhaoyun;Li Lilian;Ding Kai;Wang Guojin;Song Jia;Fu Rong
5 Abnormal expression and mutation of the RBPJ gene may be involved in CD59(-) clonal proliferation in paroxysmal nocturnal hemoglobinuria 期刊论文 Li Liyan;Liu Hui;Wang Honglei;Liu Zhaoyun;Chen Yingying;Li Lijuan;Song Jia;Wang Guojin;Fu Rong
6 Complement C3a activates osteoclasts by regulating the PI3K/PDK1/SGK3 pathway in patients with multiple myeloma 期刊论文 Fengjuan Jiang;Hui Liu;Fengping Peng;Zhaoyun Liu;Kai Ding;Jia Song;Lijuan Li;Jin Chen;Qing Shao;Siyang Yan;Kim De Veirman;Karin Vanderkerken;Rong FU
7 阵发性睡眠性血红蛋白尿症抗补体治疗现状 期刊论文 付蓉
8 Analysis of clinical characteristics of 92 patients with paroxysmal nocturnal hemoglobinuria: A single institution experience in China 期刊论文 Fu Rong;Li Liyan;Li Lijuan;Li Hui;Zhang Tian;Ding Shaoxue;Wang Guojin;Song Jia;Wang Huaquan;Xing Limin;Guan Jing;Shao Zonghong
9 Dose-Reduced Decitabine Might Bring Benefits for Elderly AML Patients with Complex Karyotype: a Case Report 期刊论文 Sun Yingying;Wu Chengcheng;Liu Chunyan;Shao Zonghong
10 Proteinase 3 expression on the neutrophils of patients with paroxysmal nocturnal hemoglobinuria 期刊论文 Liu Hui;Liu Yi;Li Yi;Liu Zhaoyun;Li Liyan;Ding Shaoxue;Wang Yihao;Zhang Tian;Li Lijuan;Shao Zonghong;Fu Rong
11 Th9 Cells in Peripheral Blood Increased in Patients with Immune-Related Pancytopenia 期刊论文 Shao Qing;Wang Yangyang;Liu Zhaoyun;Liu Hui;Wang Yihao;Zhao Yang;Li Lijuan;Fu Rong
12 CD56(bright) natural killer cells exhibit abnormal phenotype and function in severe aplastic anemia 期刊论文 Chen Tong;Liu ChunYan;Li LiJuan;Liu Hui;Wang Ting;Shao ZongHong;Fu Rong
13 我如何诊治阵发性睡眠性血红蛋白尿症 期刊论文 付蓉
14 Clinical observation of low-dose combination chemotherapy in refractory/recurrent paroxysmal nocturnal hemoglobinuria patients: A single-center retrospective analysis 期刊论文 Liyan Li;Hui Liu;Honglei Wang;Zhaoyun Liu;Yingying Chen;Chunyan Liu;Xiaoyu Zhao;Lijuan Li;Huaquan Wang;Zonghong Shao;Rong Fu
15 The expression and effect of Recombination signal binding protein-Jk gene in PNH patients 会议论文 Li liyan;Liu Hui;Wang Honglei;liu zhaoyun;Chen Yingying;Li Lijuan;Song Jia;Wang Guojin;Fu Rong
16 Expression of C1q in the serum of patients with non-severe aplastic anemia, and its association with disease severity 期刊论文 Ding Shaoxue;Liu Chunyan;Li Yang;Liu Hui;Liu Zhaoyun;Chen Tong;Zhang Tian;Shao Zonghong;Fu Rong
17 A Pig-a conditional knock-out mice model mediated by Vav-iCre: stable GPI-deficient and mild hemolysis 期刊论文 Yingying Chen;Hui Liu;Lijie Zeng;Liyan Li;Dan Lu;Zhaoyun Liu;Rong Fu
18 Proteomics analysis reveals alterations of NK cells in patients with severe aplastic anemia 期刊论文 Liu Hui;Zhang Tian;Chen Yingying;Liu Chunyan;Qi Weiwei;Shao Yuanyuan;Yu Hong;Chen Tong;Ding Shaoxue;Li Yang;Wang Ting;Shao Zonghong;Fu Rong
19 阵发性睡眠性血红蛋白尿症发病机制 期刊论文 李丽燕;付蓉
20 CCN1 stimulated the osteoblasts via PTEN/AKT/GSK3 beta/cyclinD1 signal pathway in Myeloma Bone Disease 期刊论文 Yan Siyang;Liu Hui;Liu Zhaoyun;Peng Fengping;Jiang Fengjuan;Li Lijuan;Fu Rong
21 Infection risk in autoimmune hematological disorders with low-dose rituximab treatment 期刊论文 Wang Honglei;Yan Siyang;Liu Hui;Li Lijuan;Song Jia;Wang Guojin;Wang Huaquan;Wu Yuhong;Shao Zonghong;Fu Rong
22 Epstein Barr Virus Infection Affects Function of Cytotoxic T Lymphocytes in Patients with Severe Aplastic Anemia 期刊论文 Zhang Tian;Liu Chunyan;Liu Hui;Li Lijuan;Wang Ting;Fu Rong
23 Clinical features and treatment outcome of elderly multiple myeloma patients with impaired renal function 期刊论文 Chen Jin;Liu Hui;Li Lijuan;Liu Zhaoyun;Song Jia;Wang Guojin;Wang Huaquan;Ruan Erbao;Ding Kai;Shao Zonghong;Fu Rong
24 Immunological characteristics and effect of cyclosporin in patients with immune thrombocytopenia 期刊论文 Ting Wang;Xin He;Ningyuan Ran;Chunyan Liu;Limin Xing;Huaquan Wang;Rong Fu;Zonghong
25 Abnormal numbers of CD4(+) T lymphocytes and abnormal expression of CD4(+) T lymphocyte-secreted cytokines in patients with immune-related haemocytopenia 期刊论文 Chen Jin;Liu Hui;Li Liyan;Wang Honglei;Li Yi;Wang Yihao;Ding Kai;Hao Shanfeng;Shao Yuanyuan;Li Lijuan;Song Jia;Wang Guojin;Shao Zonghong;Fu Rong
26 Effects of microRNA-21 on apoptosis by regulating the expression of PTEN in diffuse large B-cell lymphoma 期刊论文 Song Jia;Shao Qing;Li Chunhong;Liu Hui;Li Jing;Wang Yihao;Song Wenjing;Li Lijuan;Wang Guojin;Shao Zonghong;Fu Rong
27 SUZ12 participates in the proliferation of PNH clones by regulating histone H3K27me3 levels 期刊论文 Yingying Chen;Hui Liu;Lijie Zeng;Liyan Li;Dan Lu;Zhaoyun Liu;Rong Fu
28 LncRNA 在阵发性睡眠性血红蛋白尿症患者促进PNH克隆增殖中的作用研究 会议论文 王红蕾;付蓉
29 CTLA-4 and HLA-DQ are key molecules in the regulation of mDC-mediated cellular immunity by Tregs in severe aplastic anemia 期刊论文 Liu Bingnan;Shao Yuanyuan;Liang Xiaowei;Lu Dan;Yan Li;Churov Alexey;Fu Rong
30 Long Non-coding RNA MALAT1 Contributed to the Proliferation of PNH Clone in Paroxysmal Nocturnal Hemoglobinuria Patients 期刊论文 Honglei Wang;Yingying Chen;Hui Liu;Zhaoyun Liu;Rong FU
31 Multiple myeloma-derived exosomes inhibit osteoblastic differentiation and improve IL-6 secretion of BMSCs from multiple myeloma 期刊论文 Liu Zhaoyun;Liu Hui;Li Yanqi;Shao Qin;Chen Jin;Song Jia;Fu Rong
32 The clinical characteristics and therapy response of patients with acquired pure red cell aplasia 期刊论文 Fu Rong;Zhang Tian;Liu Bingnan;Song Jia;Wang Guojin;Li Lijuan;Wang Huaquan;Xing Limin;Wu Yuhong;Guan Jing;Shao Zonghong
33 Iron overload regulate the cytokine of mesenchymal stromal cells through ROS/HIF-1 alpha pathway in Myelodysplastic syndromes 期刊论文 Hu Jiaxin;Meng Fanqiao;Hu Xian;Huang Lei;Liu Hui;Liu Zhaoyun;Li Lijuanli
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